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DeCS
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Descriptor Inglés:
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Hereditary Autoinflammatory Diseases
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Descriptor Español:
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Enfermedades Autoinflamatorias Hereditarias
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Descriptor Portugués:
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Doenças Hereditárias Autoinflamatórias
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Sinónimos Inglés:
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Hereditary Autoinflammation Diseases
Hereditary Periodic Fever Syndromes
Hereditary Recurrent Fevers
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Categoría:
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C16.320.382
C17.800.827.368
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Definición Inglés:
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Hereditary inflammation conditions, characterized by recurrent episodes of systemic inflammation. Common symptoms include recurrent fever, rash, arthritis, fatigue, and secondary AMYLOIDOSIS. Hereditary autoinflammatory diseases are associated with mutations in genes involved in regulation of normal inflammatory process and are not caused by AUTOANTIBODIES, or antigen specific T-LYMPHOCYTES. |
Nota Histórica Inglés:
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2010 (2000); for Hereditary Periodic Fever Syndromes use Familial Mediterranean Fever 2000-2009
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Calificadores Permitidos Inglés:
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Número del Registro:
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53555
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Identificador Único:
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D056660
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Ocurrencia en la BVS:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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